Q43.1 – Hirschsprung's disease

ICD-10-CM 2027 diagnosis code · Other congenital malformations of the digestive system

Billable code

ICD-10-CM code Q43.1

Code: Q43.1 (claims format: Q431)
Description: Hirschsprung's disease
Billable: Yes – valid for HIPAA-covered transactions
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 17. Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders (Q00-QA1)
Block: Q38-Q45 Other congenital malformations of the digestive system
Parent codes: Q43

Notes for Q43.1

Applicable to:

Aganglionosis
Congenital (aganglionic) megacolon

Index terms for Q43.1

Entries in the ICD-10-CM alphabetic index that lead to this code:

Related codes in Q43

Q43.0 – Meckel's diverticulum (displaced) (hypertrophic)Billable
Q43.2 – Other congenital functional disorders of colonBillable
Q43.3 – Congenital malformations of intestinal fixationBillable
Q43.4 – Duplication of intestineBillable
Q43.5 – Ectopic anusBillable
Q43.6 – Congenital fistula of rectum and anusBillable
Q43.7 – Persistent cloacaBillable
Q43.8 – Other specified congenital malformations of intestineBillable
Q43.9 – Congenital malformation of intestine, unspecifiedBillable

Frequently asked questions

What is ICD-10 code Q43.1?

Q43.1 is the ICD-10-CM code for hirschsprung's disease, in the block Q38-Q45 (Other congenital malformations of the digestive system).

Is Q43.1 a billable code?

Yes. Q43.1 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does Q43.1 belong to?

It belongs to category Q43 – Other congenital malformations of intestine.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.