N07.1 – Hereditary nephropathy, not elsewhere classified with focal and segmental glomerular lesions

ICD-10-CM 2027 diagnosis code · Glomerular diseases

Billable code

ICD-10-CM code N07.1
Code
N07.1 (claims format: N071)
Description
Hereditary nephropathy, not elsewhere classified with focal and segmental glomerular lesions
Short description
Heredit nephrop, NEC w focal and seg glomerular lesions
Billable
Yes – valid for HIPAA-covered transactions
Valid for
Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter
14. Diseases of the genitourinary system (N00-N99)
Block
N00-N08 Glomerular diseases
Parent codes
N07

Notes for N07.1

Applicable to:
  • Hereditary nephropathy, not elsewhere classified with focal and segmental hyalinosis
  • Hereditary nephropathy, not elsewhere classified with focal and segmental sclerosis
  • Hereditary nephropathy, not elsewhere classified with focal glomerulonephritis

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

N07 – Hereditary nephropathy, not elsewhere classified

Excludes2 (not included here):
  • Alport's syndrome (Q87.81-)
  • hereditary amyloid nephropathy (E85.-)
  • nail patella syndrome (Q87.2)
  • non-neuropathic heredofamilial amyloidosis (E85.-)

Block N00-N08

Excludes1 (not coded here):
  • hypertensive chronic kidney disease (I12.-)
Code also:
  • any associated kidney failure (N17-N19).

Index terms for N07.1

Entries in the ICD-10-CM alphabetic index that lead to this code:

Related codes in N07

Frequently asked questions

What is ICD-10 code N07.1?

N07.1 is the ICD-10-CM code for hereditary nephropathy, not elsewhere classified with focal and segmental glomerular lesions, in the block N00-N08 (Glomerular diseases).

Is N07.1 a billable code?

Yes. N07.1 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does N07.1 belong to?

It belongs to category N07 – Hereditary nephropathy, not elsewhere classified.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.