N04 – Nephrotic syndrome

ICD-10-CM 2027 diagnosis code · Glomerular diseases

Non-billable header

ICD-10-CM code N04

Code: N04 (claims format: N04)
Description: Nephrotic syndrome
Billable: No – use a more specific code below
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 14. Diseases of the genitourinary system (N00-N99)
Block: N00-N08 Glomerular diseases

Billable codes under N04

N04 is a header code and cannot be used on claims. Choose the most specific code:

N04.0 – Nephrotic syndrome with minor glomerular abnormalityBillable
N04.1 – Nephrotic syndrome with focal and segmental glomerular lesionsBillable
N04.2 – Nephrotic syndrome with diffuse membranous glomerulonephritisHeader (more codes below)
N04.3 – Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritisBillable
N04.4 – Nephrotic syndrome with diffuse endocapillary proliferative glomerulonephritisBillable
N04.5 – Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritisBillable
N04.6 – Nephrotic syndrome with dense deposit diseaseBillable
N04.7 – Nephrotic syndrome with diffuse crescentic glomerulonephritisBillable
N04.8 – Nephrotic syndrome with other morphologic changesBillable
N04.9 – Nephrotic syndrome with unspecified morphologic changesBillable
N04.A – Nephrotic syndrome with C3 glomerulonephritisBillable
N04.B – Nephrotic syndrome with immune complex membranoproliferative glomerulonephritis (IC-MPGN)Header (more codes below)

Notes for N04

Includes:

congenital nephrotic syndrome
lipoid nephrosis

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

Block N00-N08

Excludes1 (not coded here):

hypertensive chronic kidney disease (I12.-)

Code also:

any associated kidney failure (N17-N19).

Frequently asked questions

What is ICD-10 code N04?

N04 is the ICD-10-CM code for nephrotic syndrome, in the block N00-N08 (Glomerular diseases).

Is N04 a billable code?

No. N04 is a header code with more specific child codes; report one of the billable codes listed above.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.