NPI Atlas

I01 – Rheumatic fever with heart involvement

ICD-10-CM 2027 diagnosis code · Acute rheumatic fever

Non-billable header

ICD-10-CM code I01

Code: I01 (claims format: I01)
Description: Rheumatic fever with heart involvement
Billable: No – use a more specific code below
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 9. Diseases of the circulatory system (I00-I99)
Block: I00-I02 Acute rheumatic fever

Billable codes under I01

I01 is a header code and cannot be used on claims. Choose the most specific code:

I01.0 – Acute rheumatic pericarditisBillable
I01.1 – Acute rheumatic endocarditisBillable
I01.2 – Acute rheumatic myocarditisBillable
I01.8 – Other acute rheumatic heart diseaseBillable
I01.9 – Acute rheumatic heart disease, unspecifiedBillable

Notes for I01

Excludes1 (not coded here):

chronic diseases of rheumatic origin (I05-I09) unless rheumatic fever is also present or there is evidence of reactivation or activity of the rheumatic process.

Index terms for I01

Entries in the ICD-10-CM alphabetic index that lead to this code:

Fever, rheumatic, active with heart involvement

Frequently asked questions

What is ICD-10 code I01?

I01 is the ICD-10-CM code for rheumatic fever with heart involvement, in the block I00-I02 (Acute rheumatic fever).

Is I01 a billable code?

No. I01 is a header code with more specific child codes; report one of the billable codes listed above.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.