C88.00 – Waldenstrom macroglobulinemia not having achieved remission

ICD-10-CM 2027 diagnosis code · Malignant neoplasms of lymphoid, hematopoietic and related tissue

Billable code

ICD-10-CM code C88.00

Code: C88.00 (claims format: C8800)
Description: Waldenstrom macroglobulinemia not having achieved remission
Billable: Yes – valid for HIPAA-covered transactions
Valid for: Dates of service October 1, 2026 – September 30, 2027 (FY2027)
Chapter: 2. Neoplasms (C00-D49)
Block: C81-C96 Malignant neoplasms of lymphoid, hematopoietic and related tissue
Parent codes: C88 › C88.0

Notes for C88.00

Applicable to:

Lymphoplasmacytic lymphoma with IgM-production, NOS
Lymphoplasmacytic lymphoma with IgM-production not having achieved remission
Lymphoplasmacytic lymphoma with IgM-production with failed remission
Macroglobulinemia (idiopathic) (primary) NOS
Macroglobulinemia (idiopathic) (primary) not having achieved remission
Macroglobulinemia (idiopathic) (primary) with failed remission
Waldenström macroglobulinemia NOS
Waldenström macroglobulinemia with failed remission

Notes inherited from parent codes

Instructional notes at a category or block level apply to every code below it.

C88 – Malignant immunoproliferative diseases and certain other B-cell lymphomas

Excludes1 (not coded here):

B-cell lymphoma, unspecified (C85.1-)
personal history of other malignant neoplasms of lymphoid, hematopoietic and related tissues (Z85.79)

C88.0 – Waldenstrom macroglobulinemia

Applicable to:

Lymphoplasmacytic lymphoma with IgM-production
Macroglobulinemia (idiopathic) (primary)

Excludes1 (not coded here):

small cell B-cell lymphoma (C83.0)

Block C81-C96

Excludes2 (not included here):

Kaposi's sarcoma of lymph nodes (C46.3)
secondary and unspecified neoplasm of lymph nodes (C77.-)
secondary neoplasm of bone marrow (C79.52)
secondary neoplasm of spleen (C78.89)

Related codes in C88.0

C88.01 – Waldenstrom macroglobulinemia, in remissionBillable

Frequently asked questions

What is ICD-10 code C88.00?

C88.00 is the ICD-10-CM code for waldenstrom macroglobulinemia not having achieved remission, in the block C81-C96 (Malignant neoplasms of lymphoid, hematopoietic and related tissue).

Is C88.00 a billable code?

Yes. C88.00 is a billable/specific code that can be used to indicate a diagnosis for reimbursement purposes.

What category does C88.00 belong to?

It belongs to category C88 – Malignant immunoproliferative diseases and certain other B-cell lymphomas.

Source: CDC/NCHS ICD-10-CM FY2027 code files, tabular list and index. Reference only – code assignment must follow the official ICD-10-CM guidelines and documentation in the medical record.