ICD-10 Code for Werdnig-Hoffmann Syndrome

The default ICD-10-CM 2027 code for werdnig-hoffmann syndrome (muscular atrophy) is G12.0 – Infantile spinal muscular atrophy, type I [Werdnig-Hoffman]. More specific codes depend on the details documented, as listed in the official index (1 codes, 1 billable).

Main code
G12.0 – Infantile spinal muscular atrophy, type I [Werdnig-Hoffman]
Billable
Yes

How to choose the right code

Start with the main term, then pick the indented subterm that matches the documentation (type, cause, site, laterality, episode of care). Always confirm the code in the tabular list: follow its Excludes1/Excludes2, “code first” and “use additional code” notes, and add a 7th character where required.

Source: CDC/NCHS ICD-10-CM FY2027 alphabetic index.