ICD-10 Code for Paraganglioma

The default ICD-10-CM 2027 code for paraganglioma is D44.7 – Neoplasm of uncertain behavior of aortic body and other paraganglia. More specific codes depend on the details documented, as listed in the official index (7 codes, 5 billable).

Main code: D44.7 – Neoplasm of uncertain behavior of aortic body and other paraganglia
Billable: Yes

Index entries for Paraganglioma

adrenal – D35.0- (header)
- malignant – C74.1- (header)
aortic body – D44.7
- malignant – C75.5
carotid body – D44.6
- malignant – C75.4
chromaffin – see also Neoplasm, benign, by site
- malignant – see Neoplasm, malignant, by site
extra-adrenal – D44.7
- malignant – C75.5
  - specified site – see Neoplasm, malignant, by site
  - unspecified site – C75.5
- specified site – see Neoplasm, uncertain behavior, by site
- unspecified site – D44.7
gangliocytic – D13.2
- specified site – see Neoplasm, benign, by site
- unspecified site – D13.2
glomus jugulare – D44.7
- malignant – C75.5
jugular – D44.7
malignant – C75.5
- specified site – see Neoplasm, malignant, by site
- unspecified site – C75.5
nonchromaffin – D44.7
- malignant – C75.5
  - specified site – see Neoplasm, malignant, by site
  - unspecified site – C75.5
- specified site – see Neoplasm, uncertain behavior, by site
- unspecified site – D44.7
parasympathetic – D44.7
- specified site – see Neoplasm, uncertain behavior, by site
- unspecified site – D44.7
specified site – see Neoplasm, uncertain behavior, by site
sympathetic – D44.7
- specified site – see Neoplasm, uncertain behavior, by site
- unspecified site – D44.7
unspecified site – D44.7

How to choose the right code

Start with the main term, then pick the indented subterm that matches the documentation (type, cause, site, laterality, episode of care). Always confirm the code in the tabular list: follow its Excludes1/Excludes2, “code first” and “use additional code” notes, and add a 7th character where required.

Source: CDC/NCHS ICD-10-CM FY2027 alphabetic index.