ICD-10 Code for Orotaciduria

The default ICD-10-CM 2027 code for orotaciduria, oroticaciduria (congenital) (hereditary) (pyrimidine deficiency) is E79.89 – Other specified disorders of purine and pyrimidine metabolism. More specific codes depend on the details documented, as listed in the official index (2 codes, 2 billable).

Main code
E79.89 – Other specified disorders of purine and pyrimidine metabolism
Billable
Yes

Index entries for Orotaciduria

How to choose the right code

Start with the main term, then pick the indented subterm that matches the documentation (type, cause, site, laterality, episode of care). Always confirm the code in the tabular list: follow its Excludes1/Excludes2, “code first” and “use additional code” notes, and add a 7th character where required.

Source: CDC/NCHS ICD-10-CM FY2027 alphabetic index.