ICD-10 Code for Menkes' Disease or Syndrome
The default ICD-10-CM 2027 code for menkes' disease or syndrome is E83.09 – Other disorders of copper metabolism. More specific codes depend on the details documented, as listed in the official index (2 codes, 2 billable).
- Main code
E83.09– Other disorders of copper metabolism- Billable
- Yes
Index entries for Menkes' disease or syndrome
- meaning maple-syrup-urine disease –
E71.0
How to choose the right code
Start with the main term, then pick the indented subterm that matches the documentation (type, cause, site, laterality, episode of care). Always confirm the code in the tabular list: follow its Excludes1/Excludes2, “code first” and “use additional code” notes, and add a 7th character where required.
Source: CDC/NCHS ICD-10-CM FY2027 alphabetic index.