ICD-10 Code for Maroteaux-Lamy Syndrome
The default ICD-10-CM 2027 code for maroteaux-lamy syndrome (mild) (severe) is E76.29 – Other mucopolysaccharidoses. More specific codes depend on the details documented, as listed in the official index (1 codes, 1 billable).
- Main code
E76.29– Other mucopolysaccharidoses- Billable
- Yes
How to choose the right code
Start with the main term, then pick the indented subterm that matches the documentation (type, cause, site, laterality, episode of care). Always confirm the code in the tabular list: follow its Excludes1/Excludes2, “code first” and “use additional code” notes, and add a 7th character where required.
Source: CDC/NCHS ICD-10-CM FY2027 alphabetic index.