ICD-10 Code for CDKL5

The default ICD-10-CM 2027 code for cdkl5 (Cyclin-Dependent Kinase-Like 5 Deficiency Disorder) is G40.42 – Cyclin-Dependent Kinase-Like 5 Deficiency Disorder. More specific codes depend on the details documented, as listed in the official index (1 codes, 1 billable).

Main code
G40.42 – Cyclin-Dependent Kinase-Like 5 Deficiency Disorder
Billable
Yes

How to choose the right code

Start with the main term, then pick the indented subterm that matches the documentation (type, cause, site, laterality, episode of care). Always confirm the code in the tabular list: follow its Excludes1/Excludes2, “code first” and “use additional code” notes, and add a 7th character where required.

Source: CDC/NCHS ICD-10-CM FY2027 alphabetic index.